″Moyamoya″ was first described in the Japanese literature in 1957 by Kudo, Suzuki and Takaku first named this disease ″Moyamoya″ which is Japanese for something hazy, like a puff of smoke-the appearance of the carotid rete on angiography. The
clinical course in those whose first symptoms occur in chidhood is different from those in whom symptoms develop in adult life. We have reviewed our case of moyamoya disease in patients admitted to Yonsei University College of Medicine and
analyzed
their age & sex distribution as well as clinical manifestations, together with brain CT and angiographic findings.
@ES The results were as follows:
1) Seventy six cases of moyamoya disease, 38 children, 38 adults were encounted during a 20-year period.
2) The male to female ratio was 1:1.4 for patients under 15 years of age and 1:1.9 for adults
3) The majority of attacks occurred in spring in both adults and children.
4) The most common chief complaint on admission was hemiparesis followed by convulsion in children, while in adults loss of consciousness & headeche were most commonly followed by hemiparesis.
5) Of the children, 94.7% showed infarction on brain CT, while 89.5% of adults had hemorrhage.
6) Bilateral occlusive of the carotid arteries was the most common site of lesions in both adults & children on cerebral angiography.
7) Firty four patients(22 children & 22 adults(57.9%) received conservative management. Encephalodurosynangiosis(EDAS) was performed on 14 chidren(36.8%) & 6 adults(15.6%).
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